Turner syndrome is a chromosomal disorder in which one of the sex chromosomes is missing or has other abnormalities. It is usually associated with short stature, gonadal dysfunction, hypotiroidism, congenital heart disease. Distinct craniofacial features in Turner syndrome include micrognatia, high arch palate and malocclusion. In this poster is presented a case of a 30 years old female patient with Turner syndrome who presented a class III malocclusion with periodontically involved teeth, and multiple carious lesions. After the initial parodontal therapy and carious lesions treatment, we decide for the orthodontic treatment. After completing the orthodontic treatment, the patient presented a class III Kennedy partially edentulous maxilla with modification 1 and a class III Kennedy partially edentulous mandible and referred for the prosthodontic treatment. The treatment plan consist in two porcelain fused to metal fixed partial dentures and restoring the incisal edges to complete the smile design improvement. Despite the physical and psychological differences and other problems that can occur in Turner syndrome, with appropriate medical care, interdisciplinary collaboration and ongoing support, a person with Turner syndrome can lead a normal and healthy life. Palabras clave: Turner syndrome, orthodontic treatment, prosthetic rehabilitation