Amelogenesis imperfecta refers to a hereditary dysplasia of the enamel. As a result of various defects, qualitatively and/ or quantitatively abnormal enamel forms, while the dental structure remains normal. The following article describes the condition and presents the case of an 8-year-old boy who was dentally reconstructed both functionally and aesthetically using the adhesive technique and machinable high performance polymer restorations. Palabras clave: Cerec, CAD/CAM technology, Amelogenesis imperfecta, hereditary enamel defects, high performance polymers